Editor-in-Chief Ufuk Demirkılıç Frequency Quarterly Abbreviation Turk J Vasc Surg Publisher Turkish National Vascular and Endovascular Surgery Society ISSN 2667-4947 E-ISSN 2667-5080

Turkish Journal of Vascular Surgery 2012 , Vol 21 , Issue 3
Skolyoz ve Spinal Kök Bası Bulgularının Eşlik Ettiği Klippel Trenaunay Sendromlu Bir Olgu
Kubilay KARABACAK, Gençer GENÇ, Serkan ÖZBEN, Mustafa SUNGUR, Murat KADAN, Faruk CİNGÖZ
1Kalp Damar Cerrahisi Kliniği, Erzurum Mareşal Çakmak Askeri Hastanesi, Erzurum
2Nöroloji Kliniği, Erzurum Mareşal Çakmak Askeri Hastanesi, Erzurum
3Nöroloji AD, Kafkas Üniversitesi Tıp Fakültesi, Kars
4Ortopedi Kliniği, Erzurum Mareşal Çakmak Askeri Hastanesi, Erzurum
5Kalp Damar Cerrahisi AD, GATA, Ankara
DOI : 10.9739/uvcd.2012-30893 Klippel Trenaunay syndrome (KTS) is a congenital vascular malformation associated with abnormal growth in the extremities. A case with KTS accompanying skeletal anomaly and nerve root compression symptoms is presented along with a review of the literature. A 31-year-old male patient, who was being followed for KTS, presented to the neurology outpatient clinic com- plaining of numbness at the left arm, low back pain, and numbness and pain spreading down both legs. Physical examination revealed port wine stain lesions, varicose veins, and an increased circum- ference and length at the left lower extremity. The patient had thoracic scoliosis with apex to the right. Neurological examination showed hypoactive biceps and triceps tendon reflexes at the left side, hypoesthesia at the left C7 dermatome, and positive Lasegue"s sign bilaterally. Cervical and lum- bar MRI showed multiple disc protrusions. It should be kept in mind that accompanying pathological conditions in KTS may include scoliosis and nerve root compression as well as visceral involvement and musculoskeletal deformities. Keywords : Klippel Trenaunay Syndrome; scoliosis; intervertebral disc disease
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